F?rt?na Sonras? Sessizlik; Bickerstaff Beyin Sap? Ensefalitli Bir Olgu

A pediatric case with Bickerstaff’s brainstem encephalitis (BBE), which is a very rare monophasic post-infectious condition characterized by central nervous system involvement, unconsciousness, ophthalmoplegia and ataxia, presented. Twelve years old patient was brought difficulty in eye movements ataxia. On the second day, she became agitated lethargic, then bulbar palsy whole body paralysis developed. Upper motor neuron involvement evident. Routine biochemical parameters serologic tests, cranial magnetic resonance imaging, lumbar puncture, autoimmune, paraneoplastic, electrophysiological studies were evaluated. All normal except for encephalopathic first electroencephalography (EEG) EEG repeated on 25th day reported to be normal. Anti-ganglioside antibody, anti-GQ1b found positive. Intravenous immunoglobulin (IVIG) started fourth day. rapid improvement seen week of IVIG treatment. She able walk week. completely 3 months. Although seven passed, our has not had any relapse or neurological deficit. We presented diagnosed as BBE treated successfully single dose intravenous Immunoglobulin. wanted emphasize that good prognosis even though it an acutely developing severe condition.